Aortic dissection is the major cause of premature morbidity and mortality in Marfan syndrome. Aortic root aneurysm or dissection and ectopia lentis are cardinal features of Marfan syndrome based on the 2010 Gent nosology. For the full diagnostic criteria, please visit MarfanDX.org.
Cardiac features that may be seen in Marfan syndrome
Medical management of aortic dilation
Surgical indication for descending/abdominal aortic repair
Management of aortic dilation in children
Learn this and more in the "Overview of Cardiac Management in Marfan Syndrome" download.